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KMID : 1034720180100020162
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Journal of Neurosonology and Neuroimaging
2018 Volume.10 No. 2 p.162 ~ p.165
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Hidden Moyamoya Disease Mimicking Reversible Cerebral Vasoconstriction Syndrome
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Lee Jae-Jung
Park Hong-Kyun
Cho Joong-Yang
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Abstract
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Moyamoya disease (MMD) is a progressive steno-occlusive disorder of the cerebral vasculature around the circle of Willis with secondary evolution of collateral vessels. In a few reported cases, MMD mimicked reversible cerebral vasoconstriction syndrome (RCVS). A 29-year-old woman experienced a sudden-onset generalized tonic-clonic seizure in the postpartum period. The initial brain magnetic resonance image showed high signal intensities in the bilateral basal ganglia and corona radiata on T2-weighted images along with severe stenosis in the bilateral distal internal carotid arteries and proximal middle and anterior cerebral arteries. The diagnosis of posterior leukoencephalopathy syndrome (PLS) combined with RCVS was established. Follow-up computed tomography angiography performed after 12 weeks showed comparable persistent stenosis without improvement. Thereafter, the diagnosis of MMD was highly suspected and further clinical history identified the same disorder in her father. Here we report a confusing case of PLS with hidden MMD mimicking RCVS.
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KEYWORD
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Moyamoya disease, Posterior leukoencephalopathy syndrome, Reversible cerebral vasoconstriction syndrome
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